Biotinidase deficiency is a rare autosomal recessive neurometabolic disorder resulting in biotin deficiency. Our patient presented with seizures and developmental delay since infancy and was started on megavitamin supplements. At 14 years. she presented with motor regression with encephalopathy after discontinuation of vitamins. https://www.lightemupsequences.com/deal-find-14K-Gold-plated-Lobster-Closure-Freshwater-Pearl-Bracelet-super-grab/